Splenic Mass and Isolated Gastric Varices: A Rare Presentation of a Neuroendocrine Tumor of the Pancreas
DOI:
https://doi.org/10.6092/1590-8577/3431Keywords:
Chromogranin A, Esophageal and Gastric Varices, Hypertension, Portal, Neuroendocrine Tumors, Splenic NeoplasmsAbstract
Context Splenic involvement in neuroendocrine pancreatic tumors is well known but rarely presents as a primary splenic mass. Case report A rare case of a neuroendocrine tumor involving the tail of the pancreas, splenic hilum and splenic flexure of the colon, forming a conglomerate mass and presenting as isolated gastric varices is described. A 75-year-old male presented with hematemesis and melena. Esophagogastroduodenoscopy revealed isolated gastric varices. A CT scan revealed a mass predominantly involving the spleen and a small part of the pancreas. Conclusion A splenic mass with isolated gastric varices should be kept in mind as one of the presentations of a pancreatic neuroendocrine tumor.
Image: Microscopy section from the spleen showing the neuroendocrine tumor.
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References
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